Cystic fibrosis

CF

Cystic fibrosis is a disease that causes thick, sticky mucus to build up in the lungs, digestive tract, and other areas of the body. It is one of the most common chronic lung diseases in children and young adults. It is a life-threatening disorder.

Cystic fibrosis

Parents can pass all kinds of different traits to their children, from blue eyes to blonde hair. Sometimes, parents can also pass the genes for certain diseases to their kids. Cystic fibrosis is one very serious inherited disease that makes it hard for children to breathe and digest food. Let's talk about cystic fibrosis. Genes are the coded instructions that tell our bodies how to operate. Usually, the code is correct and everything runs smoothly. But sometimes, the code is incorrect because of a defective gene or genes. In the case of cystic fibrosis, a faulty gene causes the body to produce an abnormally thick, sticky fluid called mucus. This mucus clogs the lungs, making it hard to breathe. It also gets stuck in the pancreas, making it harder for the body to break down and digest food. Millions of Americans carry the cystic fibrosis, or CF gene. Fortunately, most of them don't have cystic fibrosis. That's because you need to inherit one faulty gene from each parent to actually get the disease. Kids who are born with cystic fibrosis start showing signs very early. Newborns don't grow or gain weight as quickly as they should, and they don't make bowel movements because their bodies aren't digesting food properly. As these children get older, they may have symptoms like coughing and fatigue from the mucus in their lungs, and nausea and stomach pain from the mucus in their pancreas. They'll also get pneumonia and other lung infections more often than normal. So, you may now be asking, how do you know if your child has cystic fibrosis? Doctors diagnose cystic fibrosis using a blood test that looks for the CF gene. There is also a sweat test, which looks for saltier-than-normal sweat, another symptom of cystic fibrosis. Doctors may use other tests, such as a chest x-ray or upper GI series, to check for lung and bowel problems caused by CF. It's a good idea to get treated at a center that specializes in cystic fibrosis because they're up on all the latest therapies. For lung problems, treatments include inhaled medicines to open the airways, medicine to thin mucus and make it easier to cough up, and antibiotics to prevent lung infections. Some people may eventually need a lung transplant. For bowel problems, you'll need to eat a special diet that's higher in protein and calories to make up for the nutrients you're losing. You may also take vitamin supplements. The outlook for people with cystic fibrosis is better today than ever before. Thanks to new treatments, people with this disease can live well into adulthood. They can go to school, play sports, and get a job like everyone else. But because the symptoms of cystic fibrosis are so serious, it's very important to stay on top of treatment, and to call the doctor right away if symptoms get worse. Anyone with a family history of the disease may want to get screened for the CF gene before they decide to have children.
Cystic fibrosis - nutritional considerations

If you have cystic fibrosis, it's important to eat specific foods and take the right supplements. Let's talk about cystic fibrosis diet. So, why is your diet important? Cystic fibrosis is a disease that causes thick, sticky mucus to build up in your lungs and digestive tract. You need to eat high-calorie, high-protein foods throughout the day to maintain a normal weight because your disease makes it hard to get enough calories from the foods you eat. How do you get the right diet? First of all, you'll need to take a good multivitamin. Make sure it contains vitamins A, D, E, and K. You'll probably need to take pancreatic enzymes, too. These enzymes help your body absorb fat and protein. A good practice is to eat whenever you are hungry. This probably means you'll need to eat several small meals a day. Keep a variety of nutritious snacks around. Try to snack on something every hour, like cheese and crackers, muffins, or trail mix. Make an effort to eat regularly, even if it's only a few bites. Nutritional supplement milkshakes are good to keep on hand. Here's a recommended diet for someone with cystic fibrosis, Add grated cheese to your meals. Drink whole milk. Use enriched milk in cooking. Eat peanut butter. Put it on bread, use it for a dip, and cook with it. Put a teaspoon of butter on hot foods. Dab sour cream or yogurt on vegetables. Eat breaded meat, chicken, and fish. If you get the right balance of extra protein, fat, and calories, and take the right supplements, you can lead a much healthier life.
Clubbing

Clubbing may result from chronic low blood-oxygen levels. This can be seen with cystic fibrosis, congenital cyanotic heart disease, and several other diseases. The tips of the fingers enlarge and the nails become extremely curved from front to back.
Postural drainage

There are 6 to 12 positions a person with pulmonary disease may take to drain mucus from a certain part of the lungs. Another person may tap in certain areas to help loosen the mucus and allow it to be coughed out. Other ways to relieve the lung congestion of cystic fibrosis or bronchiectasis include percussion vests and inhaled aerosols.
Clubbed fingers

Clubbed fingers is a symptom of disease, often of the heart or lungs which cause chronically low blood levels of oxygen. Diseases which cause malabsorption, such as cystic fibrosis or celiac disease can also cause clubbing.
Cystic fibrosis

Cystic fibrosis is the most common cause of chronic lung disease in children and young adults, and the most common fatal hereditary disorder affecting white people in the United States.

Causes

Symptoms

Exams and Tests

Treatment

Support Groups

Outlook (Prognosis)

Possible Complications

When to Contact a Medical Professional

Prevention

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