Idiopathic pulmonary fibrosis

Idiopathic diffuse interstitial pulmonary fibrosis; IPF; Pulmonary fibrosis; Cryptogenic fibrosing alveolitis; CFA; Fibrosing alveolitis; Usual interstitial pneumonitis; UIP

Idiopathic pulmonary fibrosis is scarring or thickening of the lungs without a known cause.


Spirometry is a painless study of air volume and flow rate within the lungs. Spirometry is frequently used to evaluate lung function in people with obstructive or restrictive lung diseases such as asthma or cystic fibrosis.


Clubbing may result from chronic low blood-oxygen levels. This can be seen with cystic fibrosis, congenital cyanotic heart disease, and several other diseases. The tips of the fingers enlarge and the nails become extremely curved from front to back.

Respiratory system

Air is breathed in through the nasal passageways, travels through the trachea and bronchi to the lungs.



Exams and Tests


Support Groups

Outlook (Prognosis)

Possible Complications

When to Contact a Medical Professional